We report a case of giant extrarenal retroperitoneal angiomyolipoma mimicking liposarcoma. 我们报告一个巨大的肾脏外后腹腔血管平滑肌脂肪瘤（拟似脂肪肉瘤）病例。
ABSTRACT Purpose To study the clinicopathologic characteristics of extrarenal rhabbdoid tumor (ERRT). 摘要 目的：探讨恶性横纹肌样瘤的临床病理表现。
Extrarenal angiomyolipoma is an uncommon disease entity and is rare in the retroperitoneum. 摘要肾脏外的血管平滑肌脂肪瘤并不多见，在这类病例中源于后腹腔的更是稀少。
The calices show the same changes to a variable degree， depending on whether the renal pelvis is intrarenal or extrarenal. 肾盂根据其是肾内肾盂抑或外肾盂，而呈不同程度的同样改变。
Three weeks postoperatively KUB &IVU indicated normal kidneydevelopment, improved hydronephrosis, no intrarenal and extrarenal stricture. 术后3周KUB加IVU复查，肾脏显影正常，积水减少，无肾内外狭窄；
The parameter relating elimination rate to plasma concentration is total clearance, which equals renal clearance plus extrarenal （metabolic） clearance. 将消除速率和血浆浓度联系起来的参数就是总清除率。总清除率为肾清除率与肾外（经代谢）清除率之和。
